Search on: FIBRILLINS 
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Descriptor English:   Fibrillins 
Descriptor Spanish:   fibrilinas 
Descriptor Portuguese:   Fibrilinas 
Synonyms English:   Fibrillin  
Tree Number:   D09.400.430.875
D12.776.395.341
D12.776.860.300.400
Definition English:   A family of extracellular matrix glycoproteins that is structurally similar to LATENT TGF-BETA BINDING PROTEINS, but contain additional TGF-beta binding domains, in addition to unique domains at their N and C-terminals. Fibrillins assemble into 10-12 nm MICROFIBRILS that function in a variety of cell interactions with the EXTRACELLULAR MATRIX and developmental processes such as ELASTIC TISSUE maintenance and assembly, and the targeting of growth factors to the extracellular matrix. 
History Note English:   2017; use FIBRILLIN 1985-2016 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
BL blood CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   56519 
Unique Identifier:   D000071837 

Occurrence in VHL:
 

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