|
1 / 1
|
DeCS
|
|
 |
|
Descriptor English:
|
|
Trihexosylceramides
|
|
Descriptor Spanish:
|
|
trihexosilceramidas
|
|
Descriptor Portuguese:
|
|
Triexosilceramidas
|
|
Synonyms English:
|
|
Ceramide Trihexosides
Ceramides, Trihexosyl
Trihexosides, Ceramide
Trihexosyl Ceramides
|
|
Tree Number:
|
|
D02.065.313.906
D09.400.410.420.525.200.906
D10.390.470.675.200.906
D10.570.877.360.612.200.906
|
|
Definition English:
|
|
Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (FABRY DISEASE). |
|
Indexing Annotation English:
|
|
/biosyn /physiol permitted
|
|
History Note English:
|
|
91(79); was see under GLYCOSPHINGOLIPIDS 1979-90
|
|
Allowable Qualifiers English:
|
|
|
|
Record Number:
|
|
14680
|
|
Unique Identifier:
|
|
D014281
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|