Search on: MFN=57093 
Descriptors Found: 1
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Descriptor English:   Peroxisome-Targeting Signal 1 Receptor 
Descriptor Spanish:   receptor de la señal 1 de direccionamiento al peroxisoma 
Descriptor Portuguese:   Receptor 1 de Sinal de Orientação para Peroxissomos 
Synonyms English:   PEX5, Peroxin
PTS1 Receptor
PTS1 Receptors
Peroxin 5
Peroxin PEX5
Peroxin-5
Peroxisomal Biogenesis Factor 5
Peroxisome Receptor 1
Peroxisome Targeting Signal 1 Receptor
Receptor, PTS1
Receptors, PTS1  
Tree Number:   D12.776.157.635.750
Definition English:   A cytoplasmic receptor and peroxin that contains a series of TETRACOTIPEPTIDE REPEATS and binds to PEROXISOME TARGETING SIGNAL 1 (SKL-type). It is essential for protein import into PEROXISOMES; mutations in the PEX5 gene are associated with PEROXISOMAL DISORDERS such as ZELLWEGER SYNDROME. 
History Note English:   2018 (1995) 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
BL blood CF cerebrospinal fluid
CS chemical synthesis CH chemistry
CL classification DF deficiency
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   57093 
Unique Identifier:   D000074435 

Occurrence in VHL:
 

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DeCS