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CARBOXYLASE, PYRUVATE
Descriptors Found:
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DeCS
Descriptor
English
:
Pyruvate Carboxylase
Descriptor
Spanish
:
piruvato carboxilasa
Descriptor
Portuguese
:
Piruvato Carboxilase
Synonyms
English
:
Carboxylase, Pyruvate
Tree Number:
D08.811.464.257.500
Definition
English
:
A biotin-dependent enzyme belonging to the ligase
family
that catalyzes the addition of
CARBON DIOXIDE
to pyruvate. It is occurs in both
plants
and
animals
. Deficiency of this enzyme causes severe psychomotor retardation and
ACIDOSIS
, LACTIC in
infants
. EC 6.4.1.1.
Entry Combination - descr/qualif
English
:
Pyruvate Carboxylase
/
deficiency
use
Pyruvate Carboxylase Deficiency Disease
See Related
English
:
Pyruvate Carboxylase Deficiency Disease
History Note
English
:
74
Allowable Qualifiers
English
:
AD
administration & dosage
AE
adverse effects
AN
analysis
AI
antagonists & inhibitors
BI
biosynthesis
BL
blood
CF
cerebrospinal fluid
CS
chemical synthesis
CH
chemistry
CL
classification
DE
drug effects
EC
economics
GE
genetics
HI
history
IM
immunology
IP
isolation & purification
ME
metabolism
PK
pharmacokinetics
PD
pharmacology
PH
physiology
PO
poisoning
RE
radiation effects
ST
standards
SD
supply & distribution
TU
therapeutic use
TO
toxicity
UL
ultrastructure
UR
urine
Record Number:
12203
Unique Identifier:
D011766
Occurrence in VHL
:
Similar:
DeCS