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CAROLIS DISEASE
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DeCS
Descriptor
English
:
Caroli Disease
Descriptor
Spanish
:
enfermedad de Caroli
Descriptor
Portuguese
:
Doença de Caroli
Synonyms
English
:
Caroli Syndrome
Caroli's Disease
Caroli's Syndrome
Carolis Disease
Carolis Syndrome
Disease, Caroli
Disease, Caroli's
Syndrome, Caroli's
Tree Number:
C06.130.120.127.500
C06.198.184.500
C16.131.077.245.250
C16.131.314.184.500
C16.320.184.250
Definition
English
:
Congenital cystic
dilatation
of the intrahepatic
bile ducts
(
BILE DUCTS
, INTRAHEPATIC). It consists of 2 types: simple
Caroli disease
is characterized by bile duct
dilatation
(ectasia) alone; and complex
Caroli disease
is characterized by bile duct
dilatation
with extensive hepatic
fibrosis
and portal
hypertension
(
HYPERTENSION
, PORTAL). Benign renal tubular ectasia is associated with both types of
Caroli disease.
History Note
English
:
2004 (1993)
Allowable Qualifiers
English
:
BL
blood
CF
cerebrospinal fluid
CI
chemically induced
CL
classification
CO
complications
DI
diagnosis
DG
diagnostic imaging
DH
diet therapy
DT
drug therapy
EC
economics
EM
embryology
EN
enzymology
EP
epidemiology
EH
ethnology
ET
etiology
GE
genetics
HI
history
IM
immunology
ME
metabolism
MI
microbiology
MO
mortality
NU
nursing
PS
parasitology
PA
pathology
PP
physiopathology
PC
prevention & control
PX
psychology
RT
radiotherapy
RH
rehabilitation
SU
surgery
TH
therapy
UR
urine
VE
veterinary
VI
virology
Record Number:
30799
Unique Identifier:
D016767
Occurrence in VHL
:
Similar:
DeCS