1 / 1
|
DeCS
|
|
|
Descriptor English:
|
|
G(M1) Ganglioside
|
Descriptor Spanish:
|
|
gangliósido G(M1)
|
Descriptor Portuguese:
|
|
Gangliosídeo G(M1)
|
Synonyms English:
|
|
Ceramide, Monosialosyl Tetraglycosyl
GM1a Monosialoganglioside
Monosialoganglioside, GM1a
Monosialosyl Tetraglycosyl Ceramide
Tetraglycosyl Ceramide, Monosialosyl
|
Tree Number:
|
|
D09.400.410.420.025.475.390
D10.390.470.025.475.390
D10.570.877.360.025.475.390
|
Definition English:
|
|
A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis. |
History Note English:
|
|
86(77); was see under GANGLIOSIDES 1977-85
|
Allowable Qualifiers English:
|
|
|
Record Number:
|
|
5815
|
Unique Identifier:
|
|
D005677
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|