1 / 1
|
DeCS
|
|
|
Descriptor English:
|
|
Jaundice, Chronic Idiopathic
|
Descriptor Spanish:
|
|
ictericia idiopática crónica
|
Descriptor Portuguese:
|
|
Icterícia Idiopática Crônica
|
Synonyms English:
|
|
Chronic Idiopathic Jaundice
Chronic Idiopathic Jaundices
Dubin Johnson Syndrome
Dubin-Johnson Syndrome
Hyperbilirubinemia 2
Hyperbilirubinemia 2s
Hyperbilirubinemia II
Hyperbilirubinemia IIs
Idiopathic Jaundice, Chronic
Idiopathic Jaundices, Chronic
Jaundices, Chronic Idiopathic
Syndrome, Dubin-Johnson
|
Tree Number:
|
|
C16.320.565.300.764
C16.614.451.500.250
C18.452.648.300.764
|
Definition English:
|
|
A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract. |
Allowable Qualifiers English:
|
|
|
Record Number:
|
|
7735
|
Unique Identifier:
|
|
D007566
|
Occurrence in VHL:
|
|
|
Similar:
|
|
DeCS
|