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DeCS
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Descriptor English:
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Ciliary Motility Disorders
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Descriptor Spanish:
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trastornos de la motilidad ciliar
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Descriptor Portuguese:
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Transtornos da Motilidade Ciliar
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Synonyms English:
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Ciliary Dyskinesia
Ciliary Dyskinesia, Primary
Ciliary Dyskinesias
Ciliary Motility Disorder
Disorder, Ciliary Motility
Dyskinesia, Ciliary
Dyskinesia, Primary Ciliary
Immotile Cilia Syndrome
Immotile Cilia Syndromes
Primary Ciliary Dyskinesia
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Tree Number:
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C08.200
C09.150
C16.131.077.245.500
C16.320.184.500
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Definition English:
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Conditions caused by abnormal CILIA movement in the body, usually causing KARTAGENER SYNDROME, chronic respiratory disorders, chronic SINUSITIS, and chronic OTITIS. Abnormal ciliary beating is likely due to defects in any of the 200 plus ciliary proteins, such as missing motor enzyme DYNEIN arms. |
History Note English:
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1984; for Ciliary Dyskinesia, Primary use Kartagener Syndrome 2014-2018
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Allowable Qualifiers English:
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Record Number:
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2951
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Unique Identifier:
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D002925
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Occurrence in VHL:
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Similar:
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DeCS
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