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DeCS
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Descriptor English:
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Succinate-Semialdehyde Dehydrogenase
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Descriptor Spanish:
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succionato-semialdehído deshidrogenasa
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Descriptor Portuguese:
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Succinato-Semialdeído Desidrogenase
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Synonyms English:
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Dehydrogenase, Succinate Semialdehyde
Dehydrogenase, Succinate-Semialdehyde
Dehydrogenase, Succinic Semialdehyde
NAD(+)-Dependent Succinic Semialdehyde Dehydrogenase
Semialdehyde Dehydrogenase, Succinate
Semialdehyde Dehydrogenase, Succinic
Succinate Semialdehyde Dehydrogenase
Succinic Semialdehyde Dehydrogenase
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Tree Number:
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D08.811.682.657.163.843
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Definition English:
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An enzyme that plays a role in the GLUTAMATE and butanoate metabolism pathways by catalyzing the oxidation of succinate semialdehyde to SUCCINATE using NAD+ as a coenzyme. Deficiency of this enzyme, causes 4-hydroxybutyricaciduria, a rare inborn error in the metabolism of the neurotransmitter 4-aminobutyric acid (GABA). |
History Note English:
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2006(1980); use ALDEHYDE OXIDREDUCTASES 1977-1979
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Allowable Qualifiers English:
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Record Number:
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50619
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Unique Identifier:
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D050644
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Occurrence in VHL:
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Similar:
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DeCS
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