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DeCS
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Descriptor English:
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Gray Platelet Syndrome
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Descriptor Spanish:
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síndrome de plaquetas grises
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Descriptor Portuguese:
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Síndrome da Plaqueta Cinza
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Synonyms English:
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Gray Platelet Syndromes
Grey Platelet Syndrome
Grey Platelet Syndromes
Platelet Syndromes, Grey
Platelet alpha Granule Deficiency
Platelet alpha-Granule Deficiencies
Platelet alpha-Granule Deficiency
Syndrome, Gray Platelet
Syndrome, Grey Platelet
Syndromes, Gray Platelet
alpha-Granule Deficiencies, Platelet
alpha-Granule Deficiency, Platelet
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Tree Number:
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C15.378.140.427
C16.320.099.417
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Definition English:
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A rare, inherited platelet disorder characterized by a selective deficiency in the number and contents of platelet alpha-granules. It is associated with THROMBOCYTOPENIA, enlarged platelets, and prolonged bleeding time. |
History Note English:
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2009
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Allowable Qualifiers English:
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Record Number:
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53100
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Unique Identifier:
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D055652
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Occurrence in VHL:
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Similar:
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DeCS
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